{"id":1949,"date":"2016-09-19T06:58:49","date_gmt":"2016-09-19T06:58:49","guid":{"rendered":"http:\/\/sindromecharge.es\/index.php\/2016\/09\/19\/feder-se-une-a-la-semana-internacional-de-la-fpi\/"},"modified":"2016-09-19T06:58:49","modified_gmt":"2016-09-19T06:58:49","slug":"feder-se-une-a-la-semana-internacional-de-la-fpi","status":"publish","type":"post","link":"https:\/\/sindromecharge.es\/index.php\/2016\/09\/19\/feder-se-une-a-la-semana-internacional-de-la-fpi\/","title":{"rendered":"FEDER se une a la Semana Internacional de la FPI"},"content":{"rendered":"<p>Leemos en FEDER la siguiente noticia que os reproducimos de forma \u00edntegra: <\/p>\n<p><p>La Federaci\u00f3n Espa\u00f1ola de Enfermedades Raras (FEDER) se adhiere a la celebraci\u00f3n de la Semana Internacional de la Fibrosis Pulmonar Idiop\u00e1tica (FPI), una enfermedad pulmonar rara que afecta a entre 7.500 y 10.000 personas en Espa\u00f1a.<\/p>\n<p>\u00abSe trata de una patolog\u00eda de la que se desconoce su origen a\u00fan a d\u00eda de hoy\u00bb explica Juan Carri\u00f3n, Presidente de FEDER. Por eso, en el marco de este d\u00eda, \u00abnos queremos unir a quienes conviven con la FPI, una enfermedad que en la mitad de los casos se diagn\u00f3stica de forma err\u00f3nea y con una demora de entre 1 y 2 a\u00f1os\u00bb.<\/p>\n<p>A trav\u00e9s de esta semana y con multitud de actos por toda la geograf\u00eda espa\u00f1ola hasta finales de mes se busca poner de relieve los principales problemas a los que hace frente esta patolog\u00eda; entre ellos, el r\u00e1pido deterioro de la enfermedad: la supervivencia media es de 2 a 5 a\u00f1os desde su diagn\u00f3stico.<\/p>\n<h3><strong><span style=\"text-decoration: underline\">Sobre la FPI<\/span><\/strong><\/h3>\n<p>La Fibrosis Pulmonar Idiop\u00e1tica (FPI) es el tipo m\u00e1s frecuente de enfermedad intersticial pulmonar, que se caracteriza por un proceso de cicatrizaci\u00f3n anormal del tejido pulmonar que va sustituyendo al tejido pulmonar sano.<\/p>\n<p>Es una enfermedad cr\u00f3nica y progresiva limitada al pulm\u00f3n, siendo las causas de este proceso desconocidas, por lo que se denomina idiop\u00e1tica.<\/p>\n<p>En la fase inicial no se evidencian s\u00edntomas espec\u00edficos de la enfermedad (tos, fatiga\u2026), y no se hacen evidentes hasta que \u00e9sta ha evolucionado y gran parte del tejido pulmonar sano ha sido sustituido por tejido fibr\u00f3tico o cicatricial.<\/p>\n<p style=\"text-align: right\">19\/09\/2016.<\/p>\n<\/p>\n<p>Fuente: FEDER <a href=\"http:\/\/www.enfermedades-raras.org\/index.php\/actualidad\/noticias-eventos\/2-feder\/6717-feder-se-une-a-la-semana-internacional-de-la-fpi\" target=\"_blank\">FEDER se une a la Semana Internacional de la FPI<\/a><\/p>\n","protected":false},"excerpt":{"rendered":"<p>Leemos en FEDER la siguiente noticia que os reproducimos de forma \u00edntegra: La Federaci\u00f3n Espa\u00f1ola de Enfermedades Raras (FEDER) se adhiere a la celebraci\u00f3n de la Semana Internacional de la Fibrosis Pulmonar Idiop\u00e1tica (FPI), una enfermedad pulmonar rara que afecta a entre 7.500 y 10.000 personas en Espa\u00f1a. \u00abSe trata de una patolog\u00eda de la [&hellip;]<\/p>\n","protected":false},"author":1,"featured_media":0,"comment_status":"open","ping_status":"open","sticky":false,"template":"","format":"standard","meta":{"footnotes":"","_members_access_role":[],"_members_access_error":""},"categories":[8],"tags":[36],"class_list":["post-1949","post","type-post","status-publish","format-standard","hentry","category-noticias","tag-enfermedades-raras"],"yoast_head":"<!-- This site is optimized with the Yoast SEO plugin v27.9 - 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